Vascular anomalies associated with biliary atresia in pretransplant survey.
نویسندگان
چکیده
BILIARY atresia is the most common indication for liver transplants in children, and this disorder is associated with some congenital vascular anomalies. Complex vascular anomalies increase the technical difficulties of the operation and previously resulted in high mortality in these patients. The role of the radiologist is to define the conditions in which transplantation is high risk or contraindicated and to identify any anatomic variations that may alter the surgical approach. The purpose of this study is to define the congenital vascular abnormal conditions in biliary atresia patients that would alter the surgical procedure during transplantation.
منابع مشابه
The Role of Appendix in the Management of Biliary Atresia Associated with Bowel Atresia
Biliary atresia is characterized by the progressive obliteration of extra- and intrahepatic biliary duct system leading to the obstruction of bile flow in infancy. The cause(s) of biliary atresia remain unclear and many surgical options for bypassing the atretic segment have been described.1-3 Biliary atresia may be associated with small bowel atresia. The surgical interventions for biliary dr...
متن کاملTreatment of large cutaneous facial hemangioma with propranolol in a child with biliary atresia and esophageal varices
Introduction: Biliary atresia (BA) is the most common cause of neonatal jaundice, for which surgery is indicated. It may lead to portal hypertension and esophageal varices. Sometimes, BA is related to other congenital anomalies and malformation, while a coexistence of BA with facial hemangioma has not been reported, yet. Infantile hemangioma is a childhood benign vascular tumor. Beta bloc...
متن کاملESOPHAGEAL ATRESIA: RESULTS OF 108 CASES IN AN 11 YEAR PERIOD
From October 1977 to December 1988, 108 neonates born with esophageal atresia (EA) and/or a tracheoesophageal fistula (TEF) were treated at the Bristol Royal Hospital for Sick Children. An incidence of I :4000-4500 live births was noted. 1I2.4% had the common- type anomaly, 5.5% had pure esophageal atresia, and 6.5% had an H-type anomaly. 2.8% had upper and lower fistulae and 2.8% had uppe...
متن کاملUltrasonographic Triangular Cord Sign and Gallbladder Abnormality in Diagnosis of Biliary Atresia
Introduction: Early diagnosis of biliary atresia is very important for better outcome of treatment. Ultrasonography is one of the diagnostic tools for early differentiation of biliary atresia from other causes of neonatal cholestasis. It has been reported that triangular cord sign (TACS) in sonography is a reliable sign for diagnosis of biliary atresia. The aim of this study was to re-assess ...
متن کاملBiliary Atresia Associated with Polysplenia Syndrome, Dextrocardia, Situs Inversus Totalis and Malrotation of Intestines
Biliary atresia (BA) is a rare disease and the end result of a destructive, inflammatory cholangiopathy, leading to fibrosis and biliary cirrhosis. It is classified into syndromic variety with various congenital anomalies and non-syndromic (isolated anomaly). We present here a 1-month-old female child with the syndromic variety of BA associated with polysplenia syndrome, dextrocardia, situs inv...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید
ثبت ناماگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید
ورودعنوان ژورنال:
- Transplantation proceedings
دوره 33 7-8 شماره
صفحات -
تاریخ انتشار 2001